Cardiovascular problems

Some rare types of EDS are characterised by cardiovascular problems – the vascular type carries a risk of arterial rupture at a young age, and in cardiac-valvular EDS there are severe progressive problems of the aortic and mitral valves. In the more common hypermobile EDS, problems that can occur are mild dilation of the aortic root (unlikely to progress and doesn’t usually require treatment) and postural tachycardia syndrome. Whether there is an increased frequency of mitral valve prolapse in hEDS is controversial.

Autonomic dysfunction

Author
Dr Alan Hakim, Consultant Rheumatologist & Professor Rodney Grahame, Consultant Rheumatologist, The Hypermobility Unit, Hospital of St John and St Elizabeth, London

Summary

An overview of postural tachycardia syndrome (PoTS), an abnormality in the way the involuntary part of the nervous system functions - its symptoms, the diagnostic tests available and your treatment options.

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Video: Managing PoTS

Presenter
Dr Lesley Kavi, GP and Chairperson, PoTS UK

Summary

A discussion of postural tachycardia syndrome (PoTS) with tips on how it can be managed.

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Video: Arterial aneurysm and dissection in vascular EDS

Presenter
Professor Nigel Wheeldon, Lead Consultant Cardiologist, Regional Inherited Cardiac Conditions Service, Northern General Hospital, Sheffield

Summary

The investigation and management of arterial aneurysms and dissections in vascular EDS.

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Video: The postural tachycardia syndrome – PoTS and progress

Presenter
Professor Christopher Mathias, Professor of Neurovascular Medicine, UCL Institute of Neurology, London

Summary

Our current understanding of PoTS, a dysfunction of the autonomic (involuntary) nervous system.

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Video: Autonomic issues and EDS

Presenter
Dr David Low, Clinical Research Lead, Autonomic and Neurovascular Medicine Unit, Imperial College London

Summary

An overview of autonomic dysfunction and postural tachycardia syndrome (PoTS) in EDS.

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Video: Cardiac features of hypermobile EDS

Presenter
Dr Will Wallis, Consultant Cardiologist, Watford General Hospital

Summary

Heart complications in hEDS.

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Video: Classical EDS – a cardiac perspective

Presenter
Rachel Walker, Nurse Specialist, South Yorkshire Regional Inherited Cardiac Conditions Service

Summary

Cardiac complications in classical EDS.

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Teens and autonomic dysfunction

Author
Mayo Clinic

Summary

This booklet produced by the Mayo Clinic is aimed at teenagers but useful for anyone suffering with autonomic dysfunction. It explains what postural tachycardia syndrome is and gives tips on how you can feel better.
For more information surrounding this booklet contact Mayo Clinic http://www.mayoclinic.org/

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Link to PoTS UK

Summary

PoTS UK is a registered charity which supports and educates people with postural tachycardia syndrome and medical professionals about this little-known, debilitating condition.

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What is EDS?

Information sheets, how to get a diagnosis, advice for medical profesisonals......